[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$f9B-U5fAuwovF3g_VQoN7TU0jXJJrjH0ktys9EBEQqCA":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":42},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":6,"seoKeywords":6,"seoDescription":6,"coverVertical":6,"coverAcross":6,"introduceClassifications":14,"departments":40},8352,"小儿维生素E缺乏病",[15,20,25,30,35],{"id":16,"classification":17,"description":18,"sort":19,"diseaseId":12},141388,"概述","\u003Cp>　　近年来重点研究维生素E的抗氧化性能，证明维生素E可维持正常的生殖能力和肌肉正常代谢，维持中枢神经和视网膜等组织免受氧化损伤，维持血管系统的完整。由于维生素E缺乏引起生殖障碍，肌肉、肝脏、骨髓和脑功能异常，溶血以及渗出性素质等综合病征为维生素E缺乏症(deficiency of vitamin E)。\u003C/p>",0,{"id":21,"classification":22,"description":23,"sort":24,"diseaseId":12},141389,"症状","\u003Cp>　　常见症状：新生儿全身水肿开始以下肢、会阴、阴囊、阴茎为主，以后眼睑水肿逐渐全身出现水肿。\u003C/p>",1,{"id":26,"classification":27,"description":28,"sort":29,"diseaseId":12},141390,"检查","\u003Cp>　　检查项目：血分析、过氧化氢溶血试验、心电图、B超\u003C/p>\u003Cp>　　(1)红细胞溶血试验：红细胞与2%～2.4% H2O2保温后，溶血出来的血红蛋白量与蒸馏水保温所溶出者相比较，用百分数来表示，其值与血浆维生素E水平有一定的关系。缺乏维生素E红细胞对过氧化氢敏感性增高时,可观察到过氧化物溶血增加，可发生溶血性贫血。\u003C/p>\u003Cp>　　(2)血浆维生素E水平低：血浆生育酚水平\u003C/p>",2,{"id":31,"classification":32,"description":33,"sort":34,"diseaseId":12},141391,"鉴别","\u003Cp>　　2.Friedreich共济失调(FRDA) 患慢性胆汁淤积性肝胆管病或囊性纤维化的儿童发生维生素E缺乏综合征，其进行性神经损害的临床特征与FRDA很相似，在诊断时容易被误诊为FRDA，故此血清维生素E水平测定及基因诊断有助于两者鉴别。FRDA呈常染色体隐性遗传性疾病，疾病基因定位在8q13.1～q13.3。\u003C/p>",3,{"id":36,"classification":37,"description":38,"sort":39,"diseaseId":12},141392,"并发症","\u003Cp>　　2.脊髓小脑病 主要见于儿童,是由于无β脂蛋白血症,慢性胆汁淤积性肝胆管疾病,腹腔疾病或维生素E代谢的遗传异常而有脂肪吸收不良引起。\u003C/p>\u003Cp>　　3.神经系统病变 视网膜病、眼肌麻痹、视野障碍及幼儿认知能力和运动发育不良，用维生素E治疗可得到改善。\u003C/p>\u003Cp>　　4.颅内和内脏出血 心室内和室管膜下出血等，补充维生素E可得到改善。\u003C/p>",4,[41],"营养科",true]