[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fF4tu8PBdalsHJh0j9bPp3ll3WkcoNPd6HBmeOoHl7XQ":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":42},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":6,"seoKeywords":6,"seoDescription":6,"coverVertical":6,"coverAcross":6,"introduceClassifications":14,"departments":40},8348,"小儿巴德-吉亚利综合征",[15,20,25,30,35],{"id":16,"classification":17,"description":18,"sort":19,"diseaseId":12},141361,"概述","\u003Cp>　　Budd- Chiari综合征(BCS)又称肝静脉阻塞综合征(hepatic vein obstruction syndrome)、Chiari综合征、Rokitansky综合征、肝静脉血栓形成综合征、肝静脉反流障碍综合征等。由于某种原因而致肝静脉或(和)下腔静脉闭塞，闭塞可先发生于肝静脉而后延伸到下腔静脉，或与之相反。1970年Hirooka将本病征分为7型，但就目前手术水平，有人根据下腔静脉阻塞的特征、肝静脉受累的情况将Hirooka分型简化为4型。\u003C/p>",0,{"id":21,"classification":22,"description":23,"sort":24,"diseaseId":12},141362,"症状","\u003Cp>　　常见症状：腹痛、腹水、恶心与呕吐、腹泻、蜘蛛痣、黄疸、低血压、贫血、少尿\u003C/p>",1,{"id":26,"classification":27,"description":28,"sort":29,"diseaseId":12},141363,"检查","\u003Cp>　　检查项目：肝功能检查、腹水检查、肝脏超声检查、血管造影、腹腔镜\u003C/p>\u003Cp>　　可做腹腔镜检查、B型超声波检查。核素扫描、血管造影检查，如肝静脉造影、经皮的肝静脉造影、下腔静脉造影、选择性腹腔动脉造影等。\u003C/p>",2,{"id":31,"classification":32,"description":33,"sort":34,"diseaseId":12},141364,"并发症","\u003Cp>本病由于有肝静脉的阻塞，可并发肝静脉、下腔静脉血栓，静脉先天性发育异常，闭塞性静脉炎。\u003C/p>\u003Cp>1.闭塞性静脉炎：肝静脉鼻塞后可造成门脉压力的增高，侧支循环受阻，可导致腹水形成以及食管胃底静脉曲张、脐部的水母状静脉放射样改变。\u003C/p>\u003Cp>2. 下腔静脉血栓：由于下腔静脉的回流受阻，故可形成下腔静脉的分支扩张，同时可出现下肢下垂部位的水肿。\u003C/p>",3,{"id":36,"classification":37,"description":38,"sort":39,"diseaseId":12},141365,"治疗","\u003Cp>　　(一)治疗\u003C/p>\u003Cp>　　可采用如手指或导管的直接破膜术等根除性和各种门-体静脉转流或断流术等非根除性手术。不能手术者则应设法减少腹水，可利用利尿剂或行腹不超滤回输，但效果是暂时性的。1976年曾有用肝移植治疗成功之报道。\u003C/p>\u003Cp>　　(二)预后\u003C/p>\u003Cp>　　急性型者出现急腹症后几天，迅速死于休克或肝性脑病;慢性者的预后决定于病因、闭塞的部位、程度，以及能否经手术得到纠正，一般可存活数月至数年。\u003C/p>",4,[41],"营养科",true]