[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$f-CMYfbfnFzovLTxZIYgdX7vCEREIrSjbzZG6iGUc60s":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":57},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":6,"seoKeywords":6,"seoDescription":6,"coverVertical":6,"coverAcross":6,"introduceClassifications":14,"departments":55},7774,"粒-单核细胞白血病",[15,20,25,30,35,40,45,50],{"id":16,"classification":17,"description":18,"sort":19,"diseaseId":12},119054,"概述","\u003Cp>　　单核细胞白血病(monocytic leukemia) 的特异性皮肤损害为紫色到红褐色丘疹，结节和斑块，急性单核细胞白血病(AMOL)可发生水疱性损害。皮损发展周期快，可自然消退。\u003C/p>",0,{"id":21,"classification":22,"description":23,"sort":24,"diseaseId":12},119055,"病因","\u003Cp>　　CMML的发病率约为1～2/100000/年，发病中位年龄65～75岁，男女发病比例约1.5～3：1。具体病因不明，电离辐射、职业、环境致癌物质和毒物可能与本病有关。该病是骨髓造血干细胞克隆性疾病，CMML患者最常见的重现性染色体异常有+8、-7/del(7q)，和12p结构异常，约40%的患者为在确认时或疾病过程中有Ras基因点突变。\u003C/p>",1,{"id":26,"classification":27,"description":28,"sort":29,"diseaseId":12},119056,"症状","\u003Cp>　　常见症状：皮肤损害为紫色到红褐色丘疹、结节、斑块、齿龈溃疡、坏死、出血、贫血\u003C/p>\u003Cp>　　单核细胞白血病(monocytic leukemia)的特异性皮肤损害为紫色到红褐色丘疹，结节和斑块(图1)，急性单核细胞白血病(AMOL)可发生水疱性损害，皮损遍发全身并可侵犯颜面和头部，皮损发展周期快，可自然消退，白血病性齿龈增生为AMOL的特点，发生于60%的患者中，偶可发生齿龈溃疡，坏死和出血，先天性单核细胞白血病为一罕见型。\u003C/p>",2,{"id":31,"classification":32,"description":33,"sort":34,"diseaseId":12},119057,"检查","\u003Cp>　　检查项目：血常规、骨髓穿刺检查、凝血功能检查\u003C/p>\u003Cp>　　实验室检查：血常规检查具有多样性。常常表现为贫血和白细胞增高，主要是粒细胞和单核细胞增高，外周血单核细胞绝对数>10×109/L，可出现幼稚单核细胞。粒细胞常出现成熟粒细胞增多，有或无粒系发育异常，可见未成熟的粒细胞。部分病人也可以出现粒细胞减少。多数患者血小板降低，但也有部分病人血小板计数正常或增高。骨髓穿刺检查，增生程度相差较大，多数为明显活跃或极度活跃，也有增生低下者。粒细胞和单核细胞增多。原始粒细胞多>5%，原幼单核细胞也>5%，但二者之和\u003C20%。红系及巨核系增生减低。三系均有不同程度的病态造血，其中红系的典型表现为巨幼样变、核碎裂、花瓣样核、多核红细胞，成熟红细胞嗜碱性点彩。粒系病态造血表现为颗粒减少、核分叶过少(P?H畸形)、胞浆中出现空泡等，颗粒过多作为一种病态表现，特异性较差。巨核系典型的病态造血为小巨核细胞、淋巴样巨核细胞、单圆核巨核细胞、多圆核巨核细胞。\u003C/p>\u003Cp>　　血浆和尿溶菌酶含量是几乎总高的。这种溶菌酶是由单核细胞分泌的，并与单核细胞在体内的数量成正比。\u003C/p>",3,{"id":36,"classification":37,"description":38,"sort":39,"diseaseId":12},119058,"鉴别","\u003Cp>　　根据临床表现，皮损特点，组织病理，组织化学和免疫组化的特征性即可诊断。\u003C/p>",4,{"id":41,"classification":42,"description":43,"sort":44,"diseaseId":12},119059,"并发症","\u003Cp>　　并发支气管炎、肺部感染;肝、脾、淋巴结肿大;湿疹样皮疹、化脓性皮疹;由于血小板减少而发生出血。\u003C/p>",5,{"id":46,"classification":47,"description":48,"sort":49,"diseaseId":12},119060,"预防","\u003Cp>　　本病暂无有效预防措施，早发现早诊断是本病防治的关键。\u003C/p>",6,{"id":51,"classification":52,"description":53,"sort":54,"diseaseId":12},119061,"治疗","\u003Cp>　　特异性皮损可用放射线治疗和局部化疗或化疗。\u003C/p>",7,[56],"血液内科",true]