[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fXK9FJVTXjJa_DYQpOdSEjjQ511hoHprZqBXYTqpT7cA":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":60},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":58},6815,"C5功能不全综合征"," c5功能不全综合征，症状及治疗指南 - 专业医疗信息"," c5功能不全综合征, c5综合征, c5功能缺陷, 中枢神经系统疾病, 颈椎损伤, 脊髓疾病, 医学信息"," 了解c5功能不全综合征的详细信息，包括症状、诊断方法和治疗方案。此页面提供全面的医学资料，帮助您深入了解该综合征对中枢神经系统和颈椎的影响，以及应对和管理策略。",[18,23,28,33,38,43,48,53],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},116207,"概述","\u003Cp>　　C5功能不全综合征又称家族性C5功能缺陷，是Miller于1968年首先报道。主要见于婴儿，特征是血清中C5含量虽然正常，但功能缺陷。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},116208,"病因","\u003Cp>　　常染色体异常为显性或隐性遗传尚未定论有家族性发病趋势。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},116209,"症状","\u003Cp>　　常见症状：免疫力下降、腹泻、消瘦\u003C/p>\u003Cp>　　从婴儿期即出现皮脂渗出性皮炎，且可由任何部位开始很快波及全身，同时伴有慢性腹泻、消瘦、生活能力低下，由于患者抗感染能力差，很容易出现反复的细菌性感染(以革兰阴性菌为主)如中耳炎肺炎肠炎。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},116210,"检查","\u003Cp>　　检查项目：血清补体C5含量、血象、电解质检查、肾功能检查、尿检、颅脑CT\u003C/p>\u003Cp>　　血清总补体(CH50)及C5含量、泳动度及抗原均在正常范围，C5活力下降，患儿的血清不能像正常人一样有增强吞噬细胞对淀粉颗粒和葡萄球菌的吞噬作用。患儿的其他中性粒细胞功能正常，但部分病例可伴有T细胞功能异常和高球蛋白血症。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},116211,"并发症","\u003Cp>　　严重时可并发剥脱性渗出性皮炎、脓毒血症、化脓性脑膜炎等。 　　\u003C/p>",4,{"id":44,"classification":45,"description":46,"sort":47,"diseaseId":12},116212,"预防","\u003Cp>　　忌过度劳累，可适当锻炼。体育锻炼的目的在于提高机体抗病能力，促进病体康复。可结合自身的具体情况，选择适宜的锻炼方式， 但运动量不宜过大，须每天坚持，持之以恒，才能收到良好的效果。\u003C/p>",5,{"id":49,"classification":50,"description":51,"sort":52,"diseaseId":12},116213,"治疗","\u003Cp>　　以预防和控制感染为主，可根据病原菌和药物敏感实验，选用最合适的抗生素。可输新鲜血或血浆，但需每2周1次，每次10～20ml/kg。由于部分患者的T 细胞功能存在缺陷，这类病儿输入新鲜或冰冻血浆时可发生严重移植物抗宿主反应，所以在输血浆时应先测患儿的细胞免疫功能是否正常。\u003C/p>",6,{"id":54,"classification":55,"description":56,"sort":57,"diseaseId":12},116214,"饮食","\u003Cp>　　C5功能不全综合征饮食保健主要是清淡饮食，保证正常身体代谢所需的营养物质的需要，可以适当增加水果和蔬菜的摄入，但要注意避免吃辛辣刺激性食物和鸡蛋、奶、鱼虾等容易引起过敏的食物。保健方面要注意预防皮肤损害处的感染，避免搔抓，避免日晒。要积极配合医生进行治疗，做好皮损的护理。\u003C/p>",7,[59],"血液内科",true]