[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fX8STGUj3dTROZrh-OgkpLoAe7KXyDjpMAOQwKnmsiVA":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":61},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":58},6768,"高脂蛋白血症Ⅰ型"," 高脂蛋白血症ⅰ型 - 症状、原因及治疗方法\n"," 高脂蛋白血症ⅰ型, 高脂蛋白血症, 症状, 原因, 治疗方法, 血脂异常, 脂质代谢疾病, 高脂血症\n"," 高脂蛋白血症ⅰ型是一种罕见的遗传性血脂异常疾病，主要表现为血液中甘油三酯异常升高。了解高脂蛋白血症ⅰ型的症状、原因及有效的治疗方法，帮助患者更好地管理和控制病情。",[18,23,28,33,38,43,48,53],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},105268,"概述","\u003Cp>　　高脂蛋白血症Ⅰ型(外源性高三酰甘油血症;家族性脂肪诱发脂血症;高乳糜微粒血症)为一种相对较罕见的遗传性疾患，由脂蛋白脂酶或脂酶作用蛋白apo-Ⅱ功能障碍所致，引起乳糜微粒和VLDL、三酰甘油从血中清除功能下降。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},105269,"病因","\u003Cp>由遗传性脂蛋白代谢障碍引起的综合征。系常染色体隐性遗传。\u003C/p>\u003Cp>　\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},105270,"症状","\u003Cp>　　常见症状：腹痛、有黄色瘤、肝肿大、脾肿大\u003C/p>\u003Cp>　　儿童和青年人表现为胰腺炎的腹痛，带粉红色的黄色的脂肪沉积皮疹(黄色瘤)，特别多见于受压部位及伸肌表面;还可表现为视网膜质斑及肝脾肿大。多脂肪饮食可使血循环的乳糜微粒积聚从而使症状体征加重。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},105271,"检查","\u003Cp>　　检查项目：血脂检查、彩超、局部组织活检\u003C/p>\u003Cp>　　三酰甘油的显著升高可使血浆呈乳状样，乳糜微粒折射光产生乳状样，放置4℃，24小时则在血浆中有一层乳油状物积聚，这层乳油状物覆盖在澄清的血浆上具有诊断价值。脂蛋白脂酶的活力在注射Ⅳ型肝素后不能恢复(肝素后的脂溶作用)。如乳油状物下的血浆是混浊的，则VLDL、三酰甘油亦升高(Ⅴ型高脂蛋白血症)。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},105272,"鉴别","\u003Cp>　　目前没有相关内容描述。\u003C/p>",4,{"id":44,"classification":45,"description":46,"sort":47,"diseaseId":12},105273,"并发症","\u003Cp>　　早发性冠心病在家族性高胆固醇血症较为常见平均发病年龄为男性45岁、女性55岁。年龄最小的患儿于18个月即发生心肌梗死。其他部位的动脉亦可发生粥样硬化。如颈动脉发生粥样硬化可引起颈动脉狭窄，体检时在颈动脉部位可听到血管杂音。对于明显的高甘油三酯血症可引起急性胰腺炎。\u003C/p>",5,{"id":49,"classification":50,"description":51,"sort":52,"diseaseId":12},105274,"预防","\u003Cp>　　1.调整合理饮食，减少饱和脂肪酸和胆固醇的摄入。 　　2.调整生活、工作方式 积极参加体育活动、避免久坐不动，控制体重。戒烟限酒。 　　3.有冠心病、糖尿病及原发性高脂血症家族史者应每年定期做血脂、血糖、肝功能等全面检查。 　　4.40岁以上男性，绝经期后女性应每年定期做血脂全面检查。 　　5.为能够早期和及时地发现高脂血症，建议所有20岁以上的成年人，应该定期检查血浆总胆固醇水平。对于所有的胰腺炎患者，均应测定血浆三酰甘油水平。\u003C/p>",6,{"id":54,"classification":55,"description":56,"sort":57,"diseaseId":12},105275,"治疗","\u003Cp>　 针对腹部绞痛，首先要禁食，静滴等渗盐水或5%葡萄糖溶液，也可对症应用镇静或止痛药物，长期饮食应限制脂肪最高摄入量15～30g/d，脂肪应富含支链甘油三酯，血浆甘油三酯水平超过1000g/ml，可引起绞痛症，抑制食欲的制剂无效。\u003C/p>\u003Cp>　　\u003C/p>",7,[59,60],"皮肤科","内分泌科",true]