[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fzDnenG2SCm8QjYSMr_rE1nYrLbqHwA63tu41DCydWcs":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":50},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":48},5994,"小儿短指-球状晶体异位综合征"," 小儿短指-球状晶体异位综合征的病因、症状及治疗方法\n"," 小儿短指-球状晶体异位综合征, 儿童先天性疾病, 短指, 球状晶体, 眼科疾病, 临床症状, 治疗方法\n"," 了解小儿短指-球状晶体异位综合征，这种罕见的儿童先天性疾病的病因、临床症状及有效的治疗方法。帮助家长和医疗专业人士更全面地认识和管理这种复杂的疾患。",[18,23,28,33,38,43],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},38911,"概述","\u003Cp>　　短指-球状晶体异位综合征(brachy dactylia-ectopia lentis syndrome)即短指-球状晶体综合征，又名Weill-Marchesani综合征、中胚层发育异常营养障碍、先天性中胚层二形性营养不良综合征、Marchesani综合征、Marfan转化型综合征、短指-晶状体半脱位综合征、眼-短肢-短身材综合征等。因其与晶体异位蜘蛛指综合病征的特点恰恰相反，故又有“相反的马方综合征”之称。本病征为一种少见的伴有全身发育异常的遗传性疾病，继发青光眼的发生率很高，发生近视往往在儿童期，平均年龄为12.2岁。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},38913,"病因","\u003Cp>\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},38916,"症状","\u003Cp>　　常见症状：视力障碍、雾视、虹视、晶状体移位、恶心与呕吐、头痛、眼压升高、视网膜脱离、颈短、体型异常\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},38920,"检查","\u003Cp>　　检查项目：眼底检查、四肢的骨和关节平片、血常规\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},38928,"鉴别","\u003Cp>　　\u003C/p>\u003Cp>\u003C/p>",4,{"id":44,"classification":45,"description":46,"sort":47,"diseaseId":12},38932,"预防","\u003Cp>　　婚前体检在预防出生缺陷中起到积极的作用，作用大小取决于检查项目和内容，主要包括血清学检查(如乙肝病毒、梅毒螺旋体、艾滋病病毒)、生殖系统检查(如筛查宫颈炎症)、普通体检(如血压、心电图)以及询问疾病家族史、个人既往病史等，做好遗传病咨询工作。\u003C/p>\u003Cp>　　孕妇尽可能避免危害因素，包括远离烟雾、酒精、药物、辐射、农药、噪音、挥发性有害气体、有毒有害重金属等。在妊娠期产前保健的过程中需要进行系统的出生缺陷筛查，包括定期的超声检查、血清学筛查等，必要时还要进行染色体检查。\u003C/p>\u003Cp>　　一旦出现异常结果，需要明确是否要终止妊娠;胎儿在宫内的安危;出生后是否存在后遗症，是否可治疗，预后如何等等。采取切实可行的诊治措施。\u003C/p>\u003Cp>　　所用产前诊断技术有：①羊水细胞培养及有关生化检查(羊膜穿刺时间以妊娠16～20周为宜);②孕妇血及羊水甲胎蛋白测定;③超声波显像(妊娠4个月左右即可应用);④X线检查(妊娠5个月后)，对诊断胎儿骨骼畸形有利;⑤绒毛细胞的性染色质测定(受孕40～70天时)，预测胎儿性别，以帮助对X连锁遗传病的诊断;⑥应用基因连锁分析;⑦胎儿镜检查。\u003C/p>\u003Cp>　　通过以上技术的应用，防止患有严重遗传病和先天性畸形胎儿的出生。\u003C/p>",5,[49],"眼科",true]