[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$f7f4405HUNPf0pY366lh0dUNCeoLPs9JJ7ucx_7cdWoU":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":49},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":47},4348,"先天性二尖瓣闭锁"," 先天性二尖瓣闭锁的症状、诊断与治疗\n"," 先天性二尖瓣闭锁, 二尖瓣闭锁症状, 二尖瓣闭锁诊断, 二尖瓣闭锁治疗, 心脏病, 先天性心脏病, 二尖瓣疾病\n"," 了解先天性二尖瓣闭锁的详细信息，包括症状、诊断方法和治疗选择，以便有效管理和治疗这种先天性心脏病。为患者和家属提供全面的健康指导和支持。",[18,23,28,33,38,42],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},128646,"概述","\u003Cp>　　天性二尖瓣闭锁是罕见的先天性心脏畸形，患者的自然预后极差。先天性二尖瓣闭锁是指胚胎发育异常所致的二尖瓣后完全阻塞，大多数病人二尖瓣未发育而为一纤维组织膜所取代，少数系因二尖瓣叶完全融合所致。多数病人合并有主动脉瓣闭锁或发育不良。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},128647,"病因","\u003Cp>　　大多数二尖瓣闭锁患者的二尖瓣组织缺如，而为一致密坚韧的纤维组织膜取代，不能分辨正常瓣叶组织，偶有纤维膜细小仅为一纤维条索者，瓣口局部形成一隐窝。少数病人有一细小的瓣膜，但瓣口不发育，成为一瓣叶隔膜。左心室均发育不良，右心室成为主要心室腔，常明显扩大、厚。绝大多数患者合并主动脉瓣闭锁或发育不良，主动脉细小。部分病人合并有其它畸形，如右室流出道狭窄或闭锁、完全性肺静脉畸形引流、矫正型或完全性大动脉错位等。\u003C/p>\u003Cp>　　根据病理特点，可将先天性二尖瓣闭锁分为以下三个类型：\u003C/p>\u003Cp>　　1、A型者：此类型者合并主动脉瓣闭锁，左心室发育不良。大多数患者室间隔完整，少数人有小的室间隔缺损，左心室为一盲腔。此类型者最多见。\u003C/p>\u003Cp>　　2、B型者：此类型者主动脉瓣和左室发育不良，多数患者有室间隔缺损，主动脉发育较A型者为好。\u003C/p>\u003Cp>　　3、C型者：患者主动脉瓣正常，左室发育不良。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},128648,"症状","\u003Cp>　　常见症状：胸闷、口唇青紫、面色发红\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},128649,"检查","\u003Cp>　　检查项目：心电图、心脏彩超、X线片\u003C/p>",3,{"id":39,"classification":40,"description":26,"sort":41,"diseaseId":12},128650,"鉴别",4,{"id":43,"classification":44,"description":45,"sort":46,"diseaseId":12},128651,"治疗","\u003Cp>　　目前对先天性二尖瓣闭锁尚法根治。手术只能解除房间隔压力阶差并控制适当的肺血流量缓解患者症状。Mickell等主张在患儿出生后即行房间隔缺损扩大术，以防止左房压逐渐升高。为控制肺血流量可行肺动脉环缩术，对主动脉发育良好者，可施行改良Fontan术治疗。\u003C/p>",5,[48],"心血管外科",true]