[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fl7rcrydUh3sVb4ta9RPzVNV420rURS045yWExFEOMfE":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":40},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":38},3762,"小儿先天性肌强直综合征"," 小儿先天性肌强直综合征：症状、诊断与治疗\n"," 小儿先天性肌强直综合征, 肌强直症状, 儿童肌肉疾病, 先天性肌强直, 儿科肌肉病, 肌强直诊断, 肌强直治疗, 儿童健康\n"," 了解小儿先天性肌强直综合征的症状、诊断方法及治疗方案。本文提供全面的信息，帮助家长和医护人员早期识别和管理这种罕见的儿童肌肉疾病，确保儿童健康成长。",[18,23,28,33],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},23287,"概述","\u003Cp>　　肌强直综合征(myotonic syndrome)是一组较为少见的遗传性疾病，包括先天性肌强直、萎缩性强直、先天性副肌强直等疾病。其共同的特点是：随意肌主动收缩后，或给予各种机械性刺激或电刺激后，出现肌肉的强直性收缩不能立即松弛。强直性收缩的肌肉僵硬，但不伴疼痛。寒冷、兴奋、忧虑、疲劳、发热等均可使肌强直加重。用叩诊锤叩击肌肉，可出现肌球。肌电图可出现强直电位。\u003C/p>\u003Cp>　　先天性肌强直综合征(congenital myotonia syndrome)又名Thomsen病、先天性肌强直症(myotonia congenita)、强直性肌营养不良综合征、Thomsen综合征等。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},23293,"病因","\u003Cp>　　(一)发病原因\u003C/p>\u003Cp>　　本病征为常染色体显性遗传或隐性遗传。原因不明。\u003C/p>\u003Cp>　　(二)发病机制\u003C/p>\u003Cp>　　发病机制可能为神经肌肉接合处乙酰胆碱产生过多。病理上可见肌肉苍白和肥大，肌肉中肌纤维及肌质增多，一般认为是横纹肌本身的病变而无中枢及周围神经系统的异常。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},23302,"症状","\u003Cp>　　常见症状：步态蹒跚或跌倒、静立后不能起步、登楼困难\u003C/p>\u003Cp>　　令患儿用力闭目或紧握检查者手持续5s后立即放松，即可出现肌强直。反复活动多次后，肌强直逐渐减轻。用叩诊锤击大鱼际的肌肉，可引起拇指对掌而不能立即松弛。用叩诊槌叩击静止的肌肉，局部肌肉因收缩而出现凹陷，持续半分钟左右消失。三角肌及舌肌最易有此反应。肌肉活检及肌电图也有助于诊断。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},23321,"检查","\u003Cp>　　检查项目：肌电图、血清学检查\u003C/p>",3,[39],"针灸科",true]