[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fuamQyJ4yWENPABD1rj_mp23TwgCe5KXZSx2T3LVxyUQ":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":46},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":43},3148,"先天性毛细血管扩张性大理石样"," 先天性毛细血管扩张性大理石样病症详解 | 健康与治疗指南\n"," 先天性毛细血管扩张性大理石样, 毛细血管扩张, 皮肤疾病, 先天性疾病, 大理石样皮肤, 医学治疗, 皮肤保健\n"," 了解先天性毛细血管扩张性大理石样的症状和治疗方案。本指南提供详细的疾病介绍、诊断方法、治疗建议及日常护理技巧，帮助患者和家属应对这一皮肤疾病。",[18,23,28,33,38],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},159090,"概述","\u003Cp>　　本病又称先天性泛发性静脉扩张、先天性网状青斑、van Lohuizen综合征。与常染色体显性遗传有关。早期不需要治疗，对持续性的损害，可试用脉冲染料激光治疗。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},159091,"病因","\u003Cp>　　(一)发病原因\u003C/p>\u003Cp>　　主要由于毛细血管和静脉血管的畸形导致，小部分与常染色体显性遗传有关，但变异较大。最近还报道本病与母亲怀孕时体内绒毛膜促性腺激素水平的升高和短暂的胎儿腹水有关。\u003C/p>\u003Cp>　　(二)发病机制\u003C/p>\u003Cp>　　先天毛细血管和静脉血管的畸形、常染色体显性遗传导致泛发性静脉扩张。病理显示皮下毛细血管和静脉的扩张，但也有病理变化不明显或正常者。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},159092,"症状","\u003Cp>　　常见症状：动脉导管未闭、网状青斑、蜘蛛痣、挛缩性瘢痕、溃疡疼痛\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},159093,"检查","\u003Cp>　　检查项目：皮损、细胞组织化学染色、免疫病理检查、皮肤涂片显微镜检查\u003C/p>\u003Cp>临床皮肤检查：多发生于女性，出生时即存在。表现为全身性或局限性皮肤静脉网扩张，呈网状青斑，其上可产生细小溃疡，溃疡愈合后留有萎缩性瘢痕,常并发蜘蛛痣及血管角皮瘤,此现象可自然消退，亦可持续不变。另外，该病还可合并动脉导管未闭、先天性青光眼及智力低下等。\u003C/p>\u003Cp>病理学检查：活组织检查显示皮下毛细血管和静脉的扩张。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},159094,"鉴别","\u003Cp>　　1.新生儿红斑狼疮 出生后3个月内发病，头面部曝光部位受累较多，皮损常对称分布，可伴有血小板减少、轻度贫血、血清免疫学改变和肝脏肿大。\u003C/p>\u003Cp>　　2.Bockenheimer综合征 儿童期发病，一般侵犯单个肢体，表现为进行性的大静脉扩张增粗，皮下组织肿胀，可形成静脉石和血栓，患肢有增长或缩短现象。\u003C/p>",4,[44,45],"皮肤科","中西医结合科",true]