[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fa4jSU_83wzdSZHAJpLDElcrHTIcttqtsff474kJc4bo":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":46},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":43},2837,"板层状鱼鳞病"," 板层状鱼鳞病的症状、原因及治疗方法 - 全面了解板层状鱼鳞病\n"," 板层状鱼鳞病, 鱼鳞病症状, 鱼鳞病原因, 鱼鳞病治疗, 皮肤疾病, 遗传性皮肤病\n"," 全面介绍板层状鱼鳞病的症状、原因及有效治疗方法，帮助您了解这种遗传性皮肤疾病的方方面面，提供专业的健康指导。",[18,23,28,33,38],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},159181,"概述","\u003Cp>　　板层状鱼鳞病(lamellar ichthyosis)又名隐性遗传先天性鱼鳞病样红皮病(recessive congenital ichthyosis erythroderma)，是一种少见的遗传性角化性皮肤病，属常染色体隐性遗传。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},159182,"病因","\u003Cp>　　鱼鳞病的病因可归纳为几大因素：遗传、精神神经、化学、内分泌、感染因素或外份因素等等，其表皮细胞分裂率明显增加。可见此病的发病因素是多方面的，但不能什么因素和任何部位都与微循环障碍有关，我们在研究治疗药物时，着力在改善微循环上下功夫。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},159183,"症状","\u003Cp>　　常见症状：睑外翻、鳞屑、红斑(边界清楚高出皮肤)、掌跖角化过度\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},159184,"检查","\u003Cp>　　检查项目：细胞组织化学染色、免疫病理检查、涂片、皮损、眼科检查\u003C/p>\u003Cp>　　根据患者的临床皮损特点结合组织病理学检查即可明确。\u003C/p>\u003Cp>组织病理：显著角化过度，粒层存在，有些区域还可见增厚。棘层可增厚，表皮突延长，毛囊内有角朊，真皮上部血管周围有慢性炎症浸润。其他检查如下述：\u003C/p>\u003Cp>1.遗传性疾病筛查; 　　2.组织病理检查 　　(1)显性遗传性板层状鱼鳞病：表皮中度角化过度，伴颗粒层变薄或消失; 　　(2)性联寻常型板层状鱼鳞病：角化过度，颗粒层正常或稍厚; 　　(3)表皮松解角化过度板层状鱼鳞病：角化过度，表皮细胞松解，颗粒变性。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},159185,"预防","\u003Cp>　　新发现的突变位点(中国)：Q1745X，Q1790X，G2788X，Q2417X，E2422X，R2447X，R3657X。\u003C/p>",4,[44,45],"皮肤科","中西医结合科",true]