[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fKv_paQV8lTFc5wsNQTvP1XnlVqZEskuSPgNeHaxX4u8":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":47},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":43},2804,"遗传性良性上皮内角化不良"," 遗传性良性上皮内角化不良的症状、诊断与治疗 | 医学知识共享"," 遗传性良性上皮内角化不良, 角化不良, 遗传性皮肤病, 皮肤健康, 角化不良症状, 角化不良诊断, 角化不良治疗"," 了解遗传性良性上皮内角化不良的症状、诊断和治疗方法。此类遗传性皮肤病的详细解析，助您全面掌握相关知识，保障皮肤健康。",[18,23,28,33,38],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},17790,"概述","\u003Cp>　　遗传性良性上皮内角化不良(hereditary benign intraepithelial dyskeratosis)是以口腔黏膜出现无症状的白色斑片及在充血的球结膜上显现泡样，胶状的斑片为特征的先天性综合征。系常染色体显性遗传。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},17793,"症状","\u003Cp>　　常见症状：畏光、黏膜损害、细网状到斑片状的色素沉着、结膜充血\u003C/p>\u003Cp>　　根据临床表现，皮损特点，组织病理特征性即可诊断。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},17796,"检查","\u003Cp>　　检查项目：组织病理\u003C/p>\u003Cp>　　组织病理：表现为表皮增生，棘层肥厚，有含空泡的棘细胞和良性角化不良细胞。表皮是以蜡样的嗜酸性粒细胞为主。此细胞称为细胞内细胞。损害主要发生在口腔和眼部，口腔主要以颊黏膜、唇红缘，舌的下面及齿龈为主。损害呈无症状的柔软、白色海绵状皱褶可以通过口腔镜检查确诊。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},17799,"鉴别","\u003Cp>　　1.慢性疲劳综合征 (1)记忆力减退或注意力下降;(2)咽痛;(3)颈部僵直或腋窝淋巴结肿大;(4)肌肉疼痛;(5)多发性关节痛;(6)反复头痛;(7)睡眠质量不佳，醒后不轻松;(8)体力或脑力劳动后连续24小时身体不适。 　　2.白化病 可根据症状，以及通过基因检查、肿瘤标志物检查、组织病理检查鉴别。 　　3.斜视 通过眼外观检查、眼球运动检查以及视角检查等可以诊断。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},17803,"并发症","\u003Cp>　　遗传性良性上皮内角化不良并发症 　　最常见的并发症为畏光，特别是儿童最为明显，随着角膜的血管形成可发生永久性失明。同时常伴有口腔粘膜、齿龈以及舌下粘膜的损害，损害多无症状，呈现柔软的白色海绵状的皱褶。口腔的损害在出生即有或生后不久发生。眼的损害在出生后一年内均已出现，在球结膜充血的基底上发生小的类似结膜黄斑。\u003C/p>",4,[44,45,46],"眼科","皮肤科","口腔科",true]