[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$f_BrVBKKl5BXgxCOSw_fDYL3m_AzgCbPKXjgeLym7hTQ":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":57},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":53},2584,"丹吉尔病"," 丹吉尔病 - 症状、诊断、治疗全解析"," 丹吉尔病, tangier病, 稀有病, 遗传病, 高密度脂蛋白, hdl, 血脂异常"," 了解丹吉尔病的详细信息，包括其症状、诊断方法和治疗方案。作为一种罕见的遗传疾病，丹吉尔病主要影响高密度脂蛋白(hdl)的代谢，导致血脂异常。专业的医学知识为您提供全面的健康指导。",[18,23,28,33,38,43,48],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},105578,"概述","\u003Cp>　　丹吉尔病(TD)又称Tangier氏病、无α脂蛋白血症。是常染色体隐性遗传病。由于α脂蛋白合成障碍，大量胆固醇酯蓄积于网状内皮系统、肠黏膜和皮肤中。其特征为：扁桃体肥大，且有橘黄色带纹。淋巴结、肝、脾也可肿大。有的合并周围神经炎。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},105579,"病因","\u003Cp>　　常染色体隐性遗传病。由于α脂蛋白合成障碍，大量胆固醇酯蓄积于网状内皮系统、肠黏膜和皮肤中。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},105580,"症状","\u003Cp>　　常见症状：白细胞减少、角膜混浊、脾肿大、贫血、丘疹、血小板减少、硬化\u003C/p>\u003Cp>　　扁桃体肥大伴橘黄色条纹。肝、脾、淋巴结也可肿大。部分患者合并周围神经炎。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},105581,"检查","\u003Cp>　　检查项目：X线头影测量\u003C/p>\u003Cp>　　血浆高密度脂蛋白胆固醇含量低于5mg/dl，甘油三酯正常或增高，乳糜微粒减少，载脂蛋白A1消失或严重降低。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},105582,"鉴别","\u003Cp>　　与家族性高胆固醇血症、家族性高三酰甘油血症、家族性混合型高脂血症等进行鉴别。根据血脂、胆固醇水平以及详尽的体格检查鉴别并不困难。但是本病发病率极低，非常罕见。需要在排除其他相关疾病以后才考虑本病的可能性。本病表现为血清中α-脂蛋白(HDL)缺如，高胆固醇血症和高甘油三酯血症是本病的血清化特征。\u003C/p>",4,{"id":44,"classification":45,"description":46,"sort":47,"diseaseId":12},105583,"并发症","\u003Cp>　　可出现早发性动脉粥样硬化，尤其是周围血管病变较冠状动脉硬化常见。此外早发冠心病的概率也较高(男性平均40岁，女性约为50岁);掌纹条状黄色瘤等并发症。严重的可以因为HDL的缺乏导致脂肪酸、胆固醇的增高，可出现早发冠心病、心肌梗死、缺血性脑卒中等并发症。\u003C/p>",5,{"id":49,"classification":50,"description":51,"sort":52,"diseaseId":12},105584,"治疗","\u003Cp>　　无特殊疗法，扁桃体肥大引起上呼吸道梗阻时可做摘除，其组织化验检查可证明有脂类蓄积。\u003C/p>",6,[54,55,56],"皮肤科","内分泌科","病理科",true]