[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fml6i271V4_IRwXHuKdeOLYQ1bkxVKapfIiEY94NJ790":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":66},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":63},2553,"播散性黄瘤伴尿崩症"," 播散性黄瘤伴尿崩症的症状、诊断及治疗方法"," 播散性黄瘤, 尿崩症, 播散性黄瘤症状, 尿崩症治疗, 黄瘤诊断, 播散性黄瘤治疗, 黄瘤与尿崩症, 黄瘤病"," 详细介绍播散性黄瘤伴尿崩症的症状、诊断及治疗方法，帮助您了解这种罕见疾病的各个方面，包括临床表现、相关检查和治疗选择。通过本文，了解如何有效管理和治疗播散性黄瘤伴尿崩症。",[18,23,28,33,38,43,48,53,58],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},135995,"概述","\u003Cp>　　播散性黄瘤伴尿崩症是皮肤黏膜播散性黄瘤伴发尿崩症，二者特异性的结合。很少见，主要发生于幼儿和青少年。男女之比为2：1，遗传方式不明。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},135996,"病因","\u003Cp>　　该病是一种正常血脂性黄瘤病，偶有继发性高脂血症(胆固醇水平升高)发生。约50%病例伴发尿崩症。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},135997,"症状","\u003Cp>　　常见症状：播散性皮肤丘疹性黄瘤、黏膜黄瘤\u003C/p>\u003Cp>　　1.播散性皮肤丘疹性黄瘤\u003C/p>\u003Cp>　　皮损为半球形丘疹和结节状，呈暗黄色或棕黄色，它可长到豌豆大小或更大。主要对称性分布于双睑，颈部两侧及关节屈侧部，皮损可融合成疣状，变成红色或棕色。\u003C/p>\u003Cp>　　2.黏膜黄瘤\u003C/p>\u003Cp>　　皮损多发，几乎每个病例都可发生，主要见于口腔、咽后壁、鼻咽部及喉部，也可见于支气管甚或细支气管，黄瘤甚至可发生于结合膜和扁桃体。也有脑黄瘤。\u003C/p>\u003Cp>　　3.尿崩症\u003C/p>\u003Cp>　　约50%病人存在尿崩症，部分原因是对抗利尿激素的反应。尿比重有时相对较高，这种情况并不常见。\u003C/p>\u003Cp>　　脂蛋白代谢正常，甘油三酯和胆固醇水平趋于正常，但疾病过程中也可能多有升高，原因不清楚。骨髓、脑、呼吸道、心脏、肾脏、肝脏、胰腺、淋巴结、子宫及肌肉等器官均可受累。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},135998,"检查","\u003Cp>　　检查项目：组织病理\u003C/p>\u003Cp>　　最初皮损是单一形态的组织细胞增多症状，随后发展为炎性肉芽肿伴大量的白细胞、嗜酸性粒细胞、淋巴细胞及巨噬细胞浸润，最后形成富含脂质和脂蛋白的大小黄瘤细胞、Touton型巨细胞。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},135999,"鉴别","\u003Cp>　　结节性黄瘤的其他型别必须排除，如青少年黄色肉芽肿、丘疹性黄瘤及伴黄瘤样损害的组织细胞增生症X。 　\u003C/p>",4,{"id":44,"classification":45,"description":46,"sort":47,"diseaseId":12},136000,"并发症","\u003Cp>　　可见肾输尿管积水、膀胱扩张等并发症。 　　\u003C/p>",5,{"id":49,"classification":50,"description":51,"sort":52,"diseaseId":12},136001,"预防","\u003Cp>　　本病是一种正常血脂性黄瘤病偶有继发性高脂血症(胆固醇水平升高)，发生约50%病例伴发尿崩症。 　　\u003C/p>",6,{"id":54,"classification":55,"description":56,"sort":57,"diseaseId":12},136002,"治疗","\u003Cp>　　根据症状而定，皮肤黏膜结节能通过切除、电外科或液氮而去掉，可应用糖皮质激素进行系统治疗。尿崩症应同时予以抗利尿激素或安妥明治疗，刺激ADH分泌。\u003C/p>",7,{"id":59,"classification":60,"description":61,"sort":62,"diseaseId":12},136003,"饮食","\u003Cp>　　避免食用高蛋白、高脂肪辛辣和含盐过高的食品及烟酒。因为这些可使血浆渗透压升高，从而兴奋大脑口渴中枢;并且易助火生热，化燥伤阴，加重本病烦渴等症状。\u003C/p>\u003Cp>　　忌饮茶叶与咖啡。茶叶和咖啡中含有茶碱和咖啡因，能兴奋中枢神经，增强心肌收缩力，扩张肾及周围血管，而起利尿作用，使尿量增加，病情加重。\u003C/p>",8,[64,65],"皮肤科","肾病内科",true]