[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"$f65-g5LTUgHIk8dGZIHhGe2pKpxnfW0g-O4HGxk3yxcs":3,"$fTx30F1A_js0pjbjPQi_7vylbA3KPYyKwzoxfTwFl3wo":8},{"code":4,"msg":5,"message":6,"data":6,"success":7},401,"认证失败，无法访问系统资源",null,false,{"code":9,"msg":10,"message":6,"data":11,"success":66},200,"操作成功",{"id":12,"name":13,"describes":6,"symptoms":6,"checkup":6,"treatment":6,"seoTitle":14,"seoKeywords":15,"seoDescription":16,"coverVertical":6,"coverAcross":6,"introduceClassifications":17,"departments":63},1694,"Alagille综合征"," alagille综合征症状、诊断与治疗 | 什么是alagille综合征？"," alagille综合征, alagille综合征症状, alagille综合征诊断, alagille综合征治疗, 罕见遗传病, 肝病, 心血管问题"," alagille综合征是一种罕见的遗传性疾病，主要影响肝脏、心血管系统和其他器官。本页面提供详细的alagille综合征症状、诊断方法以及治疗选项的全面介绍，帮助患者及其家属更好地了解和管理这种复杂疾病。",[18,23,28,33,38,43,48,53,58],{"id":19,"classification":20,"description":21,"sort":22,"diseaseId":12},124321,"概述","\u003Cp>　　Alagille综合征是具有表型特征的慢性胆汁淤积的最常见原因，是一种累及多系统的显性遗传性疾病。该综合症在1969年由Alagille等首次报道。Alagille综合征涉及的脏器包括肝脏、心脏、骨骼、眼睛和颜面等，国外报道该病的发病率约为1/70，000。国内近年来开始关注该病。\u003C/p>",0,{"id":24,"classification":25,"description":26,"sort":27,"diseaseId":12},124322,"病因","\u003Cp>　　为先天性肝内胆管发育不良症，表现为肝脏明显肿大，显微镜下大多数门管区无胆管，有时可见发育不良的胆管，多无明显管腔，伴有明显的淤胆现象和门管区轻度纤维化，睾丸可见间质纤维化等。\u003C/p>",1,{"id":29,"classification":30,"description":31,"sort":32,"diseaseId":12},124323,"症状","\u003Cp>　　常见症状：脊柱裂、肺动脉狭窄\u003C/p>\u003Cp>　　男女均可发病，在出生后3个月内发生轻度黄疸，肝内胆汁淤积为本病的主要特征;严重瘙痒，前额突出，眼与鼻的距离大，下颏小而尖;肺动脉瓣可闻及收缩期杂音;脊椎前弓裂开，不融合，无脊柱侧突，有程度不等的智力发育迟缓;可有睾丸发育不良。\u003C/p>",2,{"id":34,"classification":35,"description":36,"sort":37,"diseaseId":12},124324,"检查","\u003Cp>　　检查项目：肝功能检查\u003C/p>\u003Cp>　　肝活检可以确诊。\u003C/p>",3,{"id":39,"classification":40,"description":41,"sort":42,"diseaseId":12},124325,"鉴别","\u003Cp>　　本征应与婴幼儿期其它胆汁淤积性疾病相鉴别。\u003C/p>",4,{"id":44,"classification":45,"description":46,"sort":47,"diseaseId":12},124326,"并发症","\u003Cp>　　在出现新生儿胆汁郁积性黄疸的AGS儿童肝脏疾病的预后较差。但是，严重的肝脏并发症可能到肝脏疾病晚期才能出现，需要终生随访。\u003C/p>",5,{"id":49,"classification":50,"description":51,"sort":52,"diseaseId":12},124327,"预防","\u003Cp>　　无特殊预防措施。服用多种药物容易产生药物交互作用，影响肝脏代谢药物能力。樟芝具有护肝解毒作用，能降低SGPT、促进肝细胞再生，提升肝脏抗氧化酵素及抑制肝组织之肝脂过氧化的能力，对于肝炎、肝硬化、肝癌患者可获得明显的改善。有肝病的人就医时，应告知医师他目前正在服用的所有药物，以做为医师处方时的参考。\u003C/p>",6,{"id":54,"classification":55,"description":56,"sort":57,"diseaseId":12},124328,"治疗","\u003Cp>　　无特殊疗法，可给予消胆胺或中药，以治疗胆汁淤积，并补充脂溶性维生素。\u003C/p>\u003Cp>　　1. 针对基础病因治疗\u003C/p>\u003Cp>　　对基本病因明确的胆汁淤积，如有可能均应力争根治或控制基础疾病。如肿瘤、结石所致的梗阻，可通过手术根治性肿瘤切除或ERCP取石;修复胆道狭窄则可使胆道引流恢复正常;对胆小管的免疫性损伤，免疫抑制剂可能有效;对药物性胆汁淤积，及时停用有关药物。\u003C/p>\u003Cp>　　2. 支持与对症治疗\u003C/p>\u003Cp>　　熊去氧胆酸、多烯磷酯酰胆碱胶囊、腺苷蛋氨酸、苯巴比妥。中药制剂有利胆退黄、降酶作用，如柴胡、白芍、茵陈、丹参等;瘙痒的治疗，可补充脂溶性维生素、钙和维生素D。\u003C/p>",7,{"id":59,"classification":60,"description":61,"sort":62,"diseaseId":12},124329,"饮食","\u003Cp>　　1.宜多食各种新鲜水果、蔬菜，进低脂肪、低胆固醇食品如：香菇、木耳、芹菜、豆芽、海带、藕、鱼肉、兔肉、鸡肉、鲜豆类等。\u003C/p>\u003Cp>　　2.宜多食干豆类及其制品。\u003C/p>\u003Cp>　　3.宜选用植物油，不用动物油。\u003C/p>\u003Cp>　　4.平时喝水时，捏少许山楂、沙棘、银杏、绞股蓝草放入水杯中当茶饮用。\u003C/p>\u003Cp>　　5.注意少吃辣椒、生蒜等刺激性食物或辛辣食品注意戒烟戒酒。\u003C/p>\u003Cp>\u003C/p>",8,[64,65],"消化内科","肝胆外科",true]